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Korean Journal of Neuromuscular Disorders ; 14 : 35 - 37, December 2022
Eyelid Myokymia as the Presenting Feature of Parry-Romberg Syndrome
Down
Jangho Cho, MD, Jangho Cho, MD, Dayoung Kim, MD, Jeeyoung Oh, MD, PhD, Kyomin Choi, MD
Department of Neurology, Konkuk University Medical Center, Seoul, Korea

Parry-Romberg syndrome is a rare acquired disease of unknown
etiology that is classically characterized by progressive atrophy
of the skin, subcutaneous tissues, and underlying bone structures.
Eyelid myokymia is a disorder of involuntary, fine, continuous,
undulating muscle fiber contractions, which is seen as a rippling
of the overlying periorbital area. We report a patient with Parry-
Romberg syndrome presenting eyelid myokymia.

KEYWORDS : Facial hemiatrophy, Myokymia, Fasciculation, Eyelids

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