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Korean Journal of Neuromuscular Disorders ; 11 : 1 - 3, December 2019 |
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A Case of Stiff-Limb Syndrome Associated with Anti-GAD65 Antibody |
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Hoseong Seo, MD, Sooyoung Kim, MD, Kee Hong Park, MD, Eun Hee Sohn, MD |
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Department of Neurology, Chungnam National University Hospital, Daejeon, Korea |
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°Á÷ÁõÈıº(stiff person syndrome)Àº ÀÚ¹ßÀû ¶Ç´Â ¿ÜºÎ ÀÚ
±Ø¿¡ ÀÇÇØ À¯¹ßµÇ´Â °Á÷(stiffness)°ú ÅëÁõ¼º ¿¬Ãà(spasm)À»
Ư¡À¸·Î ÇÏ´Â ÁúȯÀ¸·Î, ÁúȯÀÌ ÁøÇàÇÏ¸é¼ ÀÏ»ó»ýÈ° µ¿ÀÛ
¼öÇà¿¡ Àå¾Ö°¡ ¹ß»ýÇÑ´Ù.
°Á÷ÁõÈıºÀº ½Ã³À½º¿¡¼ ¾ïÁ¦ ±â´ÉÀ» ÇÏ´Â °¨¸¶¾Æ¹Ì³ëºÎƼ¸£»ê(gamma
aminobutyric acid, GABA)ÀÇ ±â´ÉÀÌ ÀúÇÏµÇ¾î ¹ß»ýÇÑ´Ù. °Á÷ÁõÈıº ȯ
ÀÚ¿¡¼ glutamic acid decarboxylase 65 (GAD65)¿¡ ´ëÇÑ Ç×ü°¡ ¹ß°ßµÇ
¸é¼, GABA ¾ïÁ¦°¡ ¸é¿ª ¹ÝÀÀ¿¡ ÀÇÇØ ³ªÅ¸³¯ °ÍÀ¸·Î ÃßÃøµÇ°í ÀÖ´Ù. °
Á÷ÇÏÁöÁõÈıº(stiff limb syndrome)Àº °Á÷
ÁõÈıºÀÇ ±¹¼ÒÀû ¾ÆÇüÀ¸·Î, °Á÷°ú ÅëÁõ¼º ¿¬ÃàÀÌ ´Ù¸®¿¡
±¹ÇѵǴ µå¹® ÁúȯÀÌ´Ù.
ÀúÀÚµéÀº GADÇ×ü ¾ç¼ºÀÎ °Á÷ÁõÈıºÀ¸·Î ÀÌ¹Ì º¸°íµÈ Áõ·ÊÀ̳ª, °Á÷Áõ
Èıº°ú ´Þ¸® ÇÏÁö¿¡ Áõ»óÀÌ ±¹ÇÑµÇ¾î °Á÷ÇÏÁöÁõÈıº¿¡ ÇÕ´çÇϸç, ¸é¿ª
Ä¡·á·Î ¼º°øÀûÀ¸·Î Ä¡·áµÇ¾ú±â¿¡ À̸¦ º¸°íÇÑ´Ù.
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